Leukoencephalopathy with neuroaxonal spheroids
Encyclopedia
Leukoencephalopathy with neuroaxonal spheroids is a special kind of leukoencephalopathy
. It is cause of severe and subacute dementia. It is inherited, following an autosomal dominant pattern
It usually presents in childhood but it can also have an adult onset. In this case, it can present MRIs that mimic those of progressive multiple sclerosis
.
Leukoencephalopathy
The term Leukoencephalopathy is a broad term for leukodystrophy-like diseases . It is applied to all brain white matter diseases, whether their molecular cause is known or not...
. It is cause of severe and subacute dementia. It is inherited, following an autosomal dominant pattern
It usually presents in childhood but it can also have an adult onset. In this case, it can present MRIs that mimic those of progressive multiple sclerosis
Multiple sclerosis
Multiple sclerosis is an inflammatory disease in which the fatty myelin sheaths around the axons of the brain and spinal cord are damaged, leading to demyelination and scarring as well as a broad spectrum of signs and symptoms...
.